Bophelo, Mafu a le Maemo
The etiology tsa sarcoidosis le seo mafu ba ferekanngoa le ho lefu Lefgrena
Lefgrena lefu - se ditshwani hilar nodes bronchopulmonary lymphatic tsamaiso e khopo ka mahlakoreng a mabeli. Lefu tsamaea le liponahatso letlalo (etymology nodosum), feberu e phahameng, 'me arthralgia. le matšoao ana ke bath ea sarcoidosis.
Ha lefu lena le ama makala a fapaneng - matšoafo, spleen, lisele tsa mmele nodes. Lefgrena lefu sarcoidosis na ha e fetisoe le hase lefu le tšoaetsanoang. Hoa lokela ho ferekanngoa le e hlophisitsweng, oncologic lefu le lefuba.
setshwantsho ea tleleniki
Sarcoidosis e bile haholo nako e telele ke lefu le sa tloaelehang, empa kajeno boemo bo fetohile, bolwetse ata ka lebelo ka potlako lefatšeng ka bophara. Ho ea ka lipalo-palo, ho feta leha e le mang e mong a utloe bohloko le lefu Lefgrena basali tloha ka ba lilemo 20 ho 40, empa lefu lena ea ka tlang ho monna leha e le ofe.
Ho ka etsahala ntle le matšoao, butle-butle kapa ka mofuta o hlobaetsang. Tleliniki Asymptomatic hangata lemoha ka tšohanyetso ka e thibelang e ka fluorography hlahloba. The atileng ka ho fetisisa ke letotong butle-butle ke lefu le bakeng sa matšoao tse latelang:
- dyspnea ka Mokhathala;
- e ache ba thotofetseng ho sefuba;
- bohloko pakeng tsa di-blades ka mahetla ;
- omileng khohlela;
- tlaase sehlopheng feberu ;
- mokhathala le bofokoli;
- ka tsela e feteletseng ho fufuleloa;
- tahlehelo ea takatso ea lijo;
- bohloko e kopanetsoeng ka morao tlaase.
Hlobaetsang bakeng sarcoidosis bitsoa lefu Lefgrena, ho e tsamaea le ho tsosa mocheso ho 38-39 ° C, bohloko e kopanetsoeng, diso letlalo ka mokgwa wa etymology, bohloko sefubeng le bokhutšoanyane phefumoloho. Ho tloaelehile ho hlobaetsang le nakong hlaphoheloa feletseng ntle le ho sebelisa ya kalafo batho bongaka le tsereletsi tse ling.
The etiology lefu lena
Ho fihlela qetellong ea phekolo e tsejoang lisosa tsa lefu lena, ho ka etsahala hore ebe qholotsa e ka lintlha tse latelang ka ntshetsa pele:
- tšoaetso, Mycobacterium lefuba, hepatitis C;
- bohloko Link lintlha, inhaling tšepe lerōle;
- ho tsuba, leo e seng motso, empa haholo di raraanyang go tsela ea lefu lena;
- lefutso.
Thibelo ea sarcoidosis
Kula lefu Lefgrena bohlokoa ke khaotse ho tsuba, ho potlakisa ho hlaphoheloa. nako ho hlokahala hore ho hlahloba makala a sefubeng sa ka lilemo tse 2. E nahane ka taba ea hore etiology ya lefu lena le lona ha le tsejoe ho fihlela qetellong, melao-motheo ea ketso e thibelang ho etsoa. Litsebi khothalletsa hore ba qobe ho kopana le tšepe lerōle le foci ea tšoaetso.
Lefgrena lefu sarcoidosis lemoha latelang extrapulmonary diriswa thulaganyou e - hlōla subcutaneous dinama tse nyenyane tse, letlalo le pheriferale lisele tsa mmele nodes. Ho na le e leng keketseho cervical, subclavian, axillary le nodes inguinal. Maemong a mang, a amehang lisele tsa mmele nodes ea mpa ea.
Bone le tsamaiso bohareng tšohile ba angoa haholo tlase hangata, empa ke matla le ho feta bakeng sa lefu lena le hlaha. Sarcoidosis ba pelo le hlaha ka 20-30% ea linyeoe tse asymptomatic. lehlakoreng le letšehali la pelo ba fokotswa ka bophahamo ba modumo, tokelo ventricle eketseha.
ho hlahloba ka hoseng 'me a kalafo fanoeng menyetla ho itšetleha ka ea hlahisa litholoana tse molemo ka. Tabeng e 'ngoe, ho na le liphetoho tse ka dinama tse nyenyane tse ea matšoafo, e ile ea qetella e isang bokooa.
Lefgrena syndrome, a hlobaetsang le sarcoidosis mothofatso
Hangata e ferekanngoa le sarcoidosis, lefuba ka lebaka la ho tšoana matšoao. Sena se hloka hore a hlahlobe ho phethahetseng, hobane bakang le phekolo e fapaneng. Tabeng se a ke ke a kopanela ho intša kalafo, haholo-holo ho nka lithethefatsi ne a rerile hore bakuli ba lefuba, seo se ka lebisa lefung.
Lefgrena lefu (a mohlala khale) - sena ke ha boemo kakaretso mokuli a se ke khotsofatsang tlhatlhobo. Ho na le liphetoho tse ka letlalo. A ka hlaha:
- papules le plaques;
- Chilblains lupus;
- keloid maqeba;
- infiltrates;
- etymology nodosum;
- SKD le CKD sarcoid Beck;
- nodes multiple teteaneng ka dinama tse nyenyane tse subcutaneous.
tlhathoba
Hlahlobo ya lefu bakuli Lefgrena ke ho phetha X-ray. E le mokhoa oa ntlafatso e sebelisa ea computed tomography. Tsamaisa skeletal le mali count ya.
The bothata ba ho kalafo ke ho thibela tshebetso a hlabang. Tsela e sebetsang hantle ka ho fetisisa ke ea ho sebelisa corticosteroids ka likhoeli tse tšeletseng. Ha e ama litho tsa ka hare ea bohlokoa e hlokahalang glucocorticosteroid hormona phekolo.
Ka potlako a tsoela pele ho 'nete hore e tšoaroa ka dithuto khutšoanyane tsamaiso intravenous ea lithethefatsi-ba khahlanong le a hlabang. Maemong a moo phekolo ke se na matla a, e neng e tšoaretsoe plasmapheresis (mali tlhoekiso). Ka matla lefu sethaleng matšoafo hloka transplants lekala. Course tsa lefu le kalafo sephetho haholo e tšoanelang, empa ho se ho hlokahala hore ho qala ho etsa joalo.
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